pleuropulmonary blastoma

1. Introduction Pleuropulmonary blastoma is a rare, exceptionally dangerous primary malignant tumor of the lung that occurs almost exclusively in infants and young children. The bottom line is that this rapidly progressing neoplasm is inextricably linked to germline mutations in the DICER1 gene and initiates as a deceptive, benign-appearing lung cyst before transforming into an … Read more